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KMID : 0357919820160040823
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Korean Journal of Pathology
1982 Volume.16 No. 4 p.823 ~ p.826
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Desmoplastic Fibroma of Femur -A case report-
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박용욱/Yong Wook Park
이계숙/이승호/유재철/송계용/안긍환/Kye Sook Lee/Sung Ho Lee/Jae Hyung Yoo/Kye Yong Song/Geung Hwan Ahn
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Abstract
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Desmoplastic fibroma of bone is rare benign tumor of fibrous tissue origin, resembling
desmoid tumor in soft tissue histologically. Jaffe (1958) first named and reported the
desmoplastic fibroma in bone. Authors experienced a case of desmoplastic fibroma in
proximal shaft of femur. A desmoplastic fibroma occurred in rib was first reported by
Ahn et al, therefore, this case was to be the second case in Korea.
A 42 years o1d woman was admitted to the Department of Orthopedic Surgery in Han
Gang Sung Sim Hospital complaining the painful swelling of right thigh after slipping
down at mountain. She noted a painful swelling of right thigh without limitation of
motion one year ago. C.B.C and blood chemistry were all within normal limits except
slightly increased alkaline phosphatase(6.0 B.U.). Urinalysis was within normal limits.
Roentgenography of right femur revealed fracture in the proximal shaft with osteolytic
and trabecular appearance of soft tissue tumor around the fracture site. Popliteal
angiogram revealed slight increase of vascularity in tumor masts. Bone scanning with
Tc99m revealed increased uptake in tumor mass.
Operative finding revealed bone fracture and large grayish white firm tumor mass in
proximal shaft of femur beneath the Vastus lateralis. The submitted specimen consisted
of a hip disarticulated lower extremity showing large eccentrically located grayish white
firm tumor mass in proximal shaft of femur, measuring 10×9.5×4㎝. in maximum
dimension. Cut surface exhibited homogenously grayish white and fibrous appearance.
Neither hemorrhage nor necrosis was noted. Microscopically the tumor was moderately
cellular, composed of interfasciculating spindle shaped fibrous tissue with rather uniform
nuclei, separates by collagenous stroma of varying amount and slit like vascular
channels. Mitotic figure was not noted. Neither osteoid nor chondroid matrix was seen
even in multiple section.
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